hnsc
 
  Home >>  Skin Conditions and Diseases >>  Ectodermal Dysplasia  
 

What is Ectodermal Dysplasia? Treatment and Cure of Dysplasia

Ectodermal dysplasia is a genetic disorder distinguished by irregular development of the skin tissues, the hair, the nails, and the jaws especially the formation of the teeth and the sweat glands. It is also alternately referred to as anhidrotic ectodermal dysplasia. Ectodermal dysplasia is placed under various classifications and the cause of this disability is due to several defective genes.

The typical type of ectodermal dysplasia is connected to the X chromosome and is known to affect only men. Another type of this disorder affects both men and women in equal numbers. This disorder greatly affects the production of sweat due to the absence or lack of sweat glands.

Young children who are afflicted with the disease have trouble in controlling their fevers. Even a tiny illness or ailment can produce a fever that is difficult to bring down, owing to the lack of sweat glands. Since sweat glands are known to control fevers through sweating and controlling the body temperature, patients with ectodermal dysplasia are at a risk of developing serious ailments.

Those affected also have chronic infections in the nasal region and heightened risk of lung disabilities. The color of the skin is usually sallow and is thin in texture. There is also deficient growth of hair and teeth and an abnormal growth of teeth is observed, amongst other abnormalities in such affected individuals. Afflicted adults are not able to endure lukewarm surroundings and require extra measures to keep a standard body temperature.

 

Types of Ectodermal Dysplasia - Risks of Dysplasia

Ectodermal dysplasia cannot be treated. There are no known treatments for Ectodermal dysplasia to prevent or cure this disorder as it stems from the genes. There are artificial methods that provide a substitute to help curb the symptoms.

Wigs, dentures can help with the cosmetic appearance of the individual while nasal sprays and artificial tears help to keep the nose and the eyes well moisturized. There is no specific treatment for this disorder. Wearing a wig and dentures can improve the child's appearance. Artificial tears may be needed to replace normal tearing and prevent drying of the eyes. It may be helpful to spray the nostrils with saline nose spray often to remove debris and prevent infection.

It is possible to live a long life even though this disorder has debilitating consequences. However care must be taken to ensure that body temperature is regulated and other symptoms are under control at all times as a neglect of ectodermal dysplasia could lead to brain damage or seizures.

 
   
/var/www/html/hnsc/templates/ectodermal-dysplasia.tplhello